Department of Pediatrics, Abass Ndao Hospital Center, Dakar, Senegal
Dr. Dieye S is a researcher in the Department of Pediatrics, Centre Hospital, University de Dakar, Senegal. He has numerous publications and Clinical Research in the areas of Pediatrics.
Research Article
Caroli Syndrome Associated with Polycystic Kidney and Congenital Heart Disease in Children in Africa
Author(s): Sow A*, Boiro D, Gueye M, Ndongo AA, Sow PS, Dieye S, Ba A, Ba I, Thiongane A, Keita Y, Dieng YJ, Deme I, Niang B, Sow NF, Seck MA, Fatah M, Diagne G, Mbaye A, Houngbadji M, Kane A, Bop K, Coundoul AM, Mbodj M, Ndiaye ST, Cisse DF, Faye PM and Ndiaye O
Caroli syndrome (CS) is defined as the association of Caroli disease with congenital liver fibrosis. It is a rare
congenital pathology with a global prevalence of less than 1 / 1,000,000 inhabitants. We report a case of CS
associated with polycystic kidney disease (PKD). He is a 7 years old boy followed from the age of 2 years for epigastric
pain. Abdominal ultrasounds were performed at the ages of 2 years, 4 years and 6 years. They showed hepatomegaly
associated with dilation of the intrahepatic bile ducts, hepatic fibrosis and bilateral renal cysts and micro-stones. The
child received several hospitalizations, the last of which was at the age of 6 years for abdominal pain, ascites, digestive
haemorrhage secondary to portal hypertension and hematuria. On admission, the weight was 19 kg (-2 DS), the size
was 119cm (-1 DS) and the BMI was 13.41 (-3DS). The child ha.. View more»