Department of Pediatrics, Abass Ndao Hospital Center, Dakar, Senegal
Dr. Coundoul AM is an Assistant professor in the Department of Pediatrics, Albert Royer National Children's Hospital in Dakar, Dakar, Senegal. The author's main area of teaching interest includes Pediatrics. He is a pediatrician in Albert Royer National Children's Hospital in Dakar
Research Article
Caroli Syndrome Associated with Polycystic Kidney and Congenital Heart Disease in Children in Africa
Author(s): Sow A*, Boiro D, Gueye M, Ndongo AA, Sow PS, Dieye S, Ba A, Ba I, Thiongane A, Keita Y, Dieng YJ, Deme I, Niang B, Sow NF, Seck MA, Fatah M, Diagne G, Mbaye A, Houngbadji M, Kane A, Bop K, Coundoul AM, Mbodj M, Ndiaye ST, Cisse DF, Faye PM and Ndiaye O
Caroli syndrome (CS) is defined as the association of Caroli disease with congenital liver fibrosis. It is a rare
congenital pathology with a global prevalence of less than 1 / 1,000,000 inhabitants. We report a case of CS
associated with polycystic kidney disease (PKD). He is a 7 years old boy followed from the age of 2 years for epigastric
pain. Abdominal ultrasounds were performed at the ages of 2 years, 4 years and 6 years. They showed hepatomegaly
associated with dilation of the intrahepatic bile ducts, hepatic fibrosis and bilateral renal cysts and micro-stones. The
child received several hospitalizations, the last of which was at the age of 6 years for abdominal pain, ascites, digestive
haemorrhage secondary to portal hypertension and hematuria. On admission, the weight was 19 kg (-2 DS), the size
was 119cm (-1 DS) and the BMI was 13.41 (-3DS). The child ha.. View more»