Department of Anesthesiology and Critical Care Medicine, Johns Hopkins University, School of Medicine, Division of Ambulatory Anesthesia, JHOC B165 Baltimore, Maryland, USA
Dr. Edward Nguyen is currently working as a Professor in the Department of Anesthesiology and Critical Care Medicine, Johns Hopkins University, School of Medicine, Division of Ambulatory Anesthesia, JHOC B165 Baltimore, Maryland, USA. His research interests related to surgery and has authored of many research articles.
Case Report
Anesthetic Considerations and Perioperative Optimization of a Patient with Hereditary Hemorrhagic Telangiectasia in the Ambulatory Surgical Setting: A Case Report
Author(s): Archana S. Hudson* and The-Hung Edward Nguyen
Hereditary Hemorrhagic Telangiectasia (HHT), also known as Osler-Weber-Rendu Syndrome, is a rare autosomal
dominant disorder characterized by multiple systemic Arteriovenous Malformations (AVMs) which presents
unique challenges and considerations for the anesthetic management during the perioperative period. Patients
with HHT are not typically considered appropriate candidates for outpatient surgery centers due to their high risk
of complications relating to these AVMs, including a higher incidence of symptomatic anemia, paradoxical air
embolus and/or bacteremia due to pulmonary AVMs, congestive heart failure, portal hypertension, seizures, and
intracranial hemorrhage. We present a case of a 55 year-old male with known history of HHT who presented to
our outpatient surgery center for intranasal mass injection/excision and septodermoplasty. Extensive planning and
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