Department of Anesthesiology and Intensive Care, Humanitas University, Milan, Italy
Case Report
End-Stage Heart Failure in Becker’s Muscular Dystrophy: A Case Report of Perioperative Management for Oncological Surgery during COVID-19 Pandemic
Author(s): Piovano Chiara*, Savi M, Babbini M, Greco M, Monzani R and Cecconi M
Background: Becker’s Muscular Dystrophy (BMD) is an X-linked recessive disease caused by dystrophin deficiency and characterized by progressive skeletal muscle weakness and functional impairment especially involving proximal muscles of the lower limbs while resulting in several comorbidities, including restrictive respiratory insufficiency and dilated cardiomyopathy.
Materials and methods: We report a case of successful intraoperative management in a 63- year- old ASA IV patient affected by BMD associated with several comorbidities who presented with ingravescent dyspnea and dysphagia due to a supraglottic laryngeal carcinoma. He is also affected by a dilated cardiomyopathy with congestive heart failure (ACC/AHA stage C), chronic atrial fibrillation and pulmonary hypertension; he carries also a Cardiac-Resynchronization Therapy-Defibri.. View more»