Journal of Surgery and Anesthesia

Abstract

Anesthesia Management in a patient with Berardenilli-Seip Congenital Lipodystrophy (BSCL) Scheduled for Open Reduction and Internal Fixation of Femur

Sami Ur Rehman*, Ahmad Farooq, Arshad Taqi and Ayesha Asad

We are presenting our case of the patient with Berardinelli-Seip Congenital Lipodystrophy (BSCL), characterized by hyperinsulinemia caused by insulin resistance combined with lipodystrophy and acromegaloid features. This patient had portal vein thrombosis, prognathosis, hypertrophic obstructive cardiomyopathy, (Left Ventricular Outflow Tract) LVOT obstruction, hyperthyroidism, hypertension and diabetes mellitus. He underwent Open Reduction and Internal Fixation (ORIF) with titanium elastic plates under spinal anesthesia.

Published Date: 2024-02-01; Received Date: 2023-12-23